Remi Kowalski

Galactose treatment of a PGM1 patient presenting with restrictive cardiomyopathy.

Sarah E Donoghue, Susan M White, Tiong Yang Tan, Remi Kowalski, Eva Morava, Joy Yaplito-Lee

Journal article  |  2021  |  JIMD Rep

We report a patient diagnosed with PGM1-CDG at 11 years of age after two biallelic likely pathogenic variants in PGM1 were found o..

Milrinone Acts as a Vasodilator But Not an Inotrope in Children After Cardiac Surgery-Insights From Wave Intensity Analysis

Sarfaraz Rahiman, Remi Kowalski, Sit Yee Kwok, Sunit Matha, Bryn Jones, Joseph J Smolich, Jonathan P Mynard, Warwick Butt, Johnny Millar

Journal article  |  2020  |  CRITICAL CARE MEDICINE

OBJECTIVES: Milrinone is an inodilator widely used in the postoperative management of children undergoing cardiac surgery. The lit..

Measurement, Analysis and Interpretation of Pressure/Flow Waves in Blood Vessels

Jonathan P Mynard, Avinash Kondiboyina, Remi Kowalski, Michael MH Cheung, Joseph J Smolich

Journal article  |  2020  |  FRONTIERS IN PHYSIOLOGY

The optimal performance of the cardiovascular system, as well as the break-down of this performance with disease, both involve com..

A Cross-Sectional Study of the Prevalence of Exercise-Induced Hypertension in Childhood Following Repair of Coarctation of the Aorta

Taryn L Luitingh, Melissa GY Lee, Bryn Jones, Remi Kowalski, Sofia Weskamp Aguero, Jane Koleff, Diana Zannino, Michael MH Cheung, Yves d'Udekem

Journal article  |  2019  |  HEART LUNG AND CIRCULATION

BACKGROUND: Exercise-testing may be a more tolerable method of detecting hypertension in children after coarctation repair compare..

Reduced Aortic Distensibility is Associated With Higher Aorto-Carotid Wave Transmission and Central Aortic Systolic Pressure in Young Adults After Coarctation Repair

Remi Kowalski, Melissa GY Lee, Lex W Doyle, Jeanie LY Cheong, Joseph J Smolich, Yves d'Udekem, Jonathan P Mynard, Michael MH Cheung

Journal article  |  2019  |  JOURNAL OF THE AMERICAN HEART ASSOCIATION

Background The long-term prognosis of patients with repaired aortic coarctation is characterized by high rates of cardiovascular a..

Comparison of invasive and non-invasive aortic wave intensity and wave power analyses in sheep

Remi Kowalski, Jonathan P Mynard, Joseph Smolich, Michael MH Cheung

Journal article  |  2019  |  PHYSIOLOGICAL MEASUREMENT

OBJECTIVE: Wave intensity (WI) and wave power (WP) analyses are powerful approaches for assessing ventricular-vascular interaction..

Noninvasive assessment of carotid arterial wave speed and distensibility

Jonathan P Mynard, Avinash Kondiboyina, Melanie M Clarke, Remi Kowalski, Michael MH Cheung, Joseph J Smolich

Journal article  |  2018  |  AMERICAN JOURNAL OF PHYSIOLOGY-HEART AND CIRCULATORY PHYSIOLOGY

Increased aortic wave reflection contributes to higher systolic blood pressure in adolescents born preterm

Remi R Kowalski, Richard Beare, Jonathan P Mynard, Jeanie LY Cheong, Lex W Doyle, Joseph J Smolich, Michael MH Cheung

Journal article  |  2018  |  JOURNAL OF HYPERTENSION

OBJECTIVE: To evaluate the wave reflection characteristics in the aortic arch and common carotid artery of ex-preterm adolescents ..

P49 QUANTIFYING WAVE REFLECTION IN CHILDREN: INVASIVE VS NON-INVASIVE CENTRAL AUGMENTATION INDEX AND REFLECTION MAGNITUDE AND THEIR ASSOCIATION WITH LEFT VENTRICULAR MASS

Jonathan Mynard, Greta Goldsmith, Remi Kowalski, Lucas Eastaugh, Geoff Lane, Gabriella Springall, Joe Smolich, Alberto Avolio, Michael Cheung

Journal article  |  2018  |  Artery Research

Robust and practical non-invasive estimation of local arterial wave speed and mean blood velocity waveforms

Remi Kowalski, Richard Beare, Marie Willemet, Jordi Alastruey, Joseph J Smolich, Michael MH Cheung, Jonathan P Mynard

Journal article  |  2017  |  PHYSIOLOGICAL MEASUREMENT

OBJECTIVE: Local arterial wave speed, a surrogate of vessel stiffness, can be estimated via the pressure-velocity (PU) and diamete..