The Chemical Chaperone, PBA, Reduces ER Stress and Autophagy and Increases Collagen IV alpha 5 Expression in Cultured Fibroblasts From Men With X-Linked Alport Syndrome and Missense Mutations
Dongmao Wang, Mardhiah Mohammad, Yanyan Wang, Rachel Tan, Lydia S Murray, Sharon Ricardo, Hayat Dagher, Tom van Agtmael, Judy Savige
Kidney International Reports | ELSEVIER SCIENCE INC | Published : 2017
Awarded by Research Councils UK Fellowship
This work was supported by grants from the Macquarie/Pederson Family Trust/Kidney Foundation of Canada/Alport Syndrome Foundation, from the Alport Syndrome Foundation of Australia to JAS, and from the Research Councils UK Fellowship (EP/E50036611) to TVA. The funding organizations played no role in the design and conduct of the study; collection, management, analysis, and interpretation of the data; nor in the preparation, review, or approval of the manuscript.