Early radiological intervention and haematology screening is associated with excellent outcomes in Budd–Chiari syndrome

Abstract

Background: Budd–Chiari syndrome (BCS) is a rare and life-threatening disorder, resulting from thrombosis of the hepatic veins. Various treatments, including pharmacological, radiological and surgical interventions, have been used. Aim: To describe retrospectively our institution's experience with management of patients with BCS. Methods: A retrospective study of all cases of primary Budd–Chiari syndrome presenting to our institution between January 2000 and August 2012 was performed. Patients with secondary Budd–Chiari syndrome due to malignancy or local mass compression were excluded. Results: Between 2000 and 2012, 27 patients with primary BCS presented with a median Rotterdam score of 1...