Journal article

Right Heart-Pulmonary Circulation Unit in Cardiomyopathies and Storage Diseases

Antonello D'Andrea, Tiziana Formisano, Andre La Gerche, Nuno Cardim, Andreina Carbone, Raffaella Scarafile, Francesca Martone, Michele D'Alto, Eduardo Bossone, Maurizio Galderisi

Heart Failure Clinics | ELSEVIER SCIENCE INC | Published : 2018


Cardiomyopathies (CM) are a heterogeneous group of muscle heart diseases, divided into 3 main categories (dilated, hypertrophic, and restrictive). In addition to these subgroups, athlete's heart and hypertensive cardiopathy are both the result of heart adaptation to increased loading conditions, making it possible to include them in the CM group. Right heart involvement is clear in some CM as arrhythmogenic CM, carcinoid syndrome, and endomyocardial fibrosis, whereas in others, like hypertrophic or dilated CM, it is known that the right heart has a prognostic impact but less clear is its pathogenic role.