Journal article
Implications of the diagnostic criteria of idiopathic pulmonary fibrosis in clinical practice: Analysis from the Australian Idiopathic Pulmonary Fibrosis Registry
HE Jo, I Glaspole, N Goh, PMA Hopkins, Y Moodley, PN Reynolds, S Chapman, EH Walters, C Zappala, H Allan, S Macansh, C Grainge, GJ Keir, A Hayen, D Henderson, S Klebe, SB Heinze, A Miller, HC Rouse, E Duhig Show all
Respirology | WILEY | Published : 2019
DOI: 10.1111/resp.13427
Abstract
Background and objective: Current guidelines for the diagnosis of idiopathic pulmonary fibrosis (IPF) provide specific criteria for diagnosis in the setting of multidisciplinary discussion (MDD). We evaluate the utility and reproducibility of these diagnostic guidelines, using clinical data from the Australian IPF Registry. Methods: All patients enrolled in the registry undergo a diagnostic review whereby international IPF guidelines are applied via a registry MDD. We investigated the clinical applicability of these guidelines with regard to: (i) adherence to guidelines, (ii) Natural history of IPF diagnostic categories and (iii) Concordance for diagnostic features. Results: A total of 417 p..
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Awarded by National Health and Medical Research Council
Funding Acknowledgements
The authors thank all the participants and physicians who contribute to the registry, as well as the registry staff who work tirelessly to gather and collate information. We also thank Alfred Health Solutions and Alfred Medical Imaging who are integral to the development and maintenance of the web-based radiology database. Lung Foundation Australia (LFA) has established the AIPFR with the generous support of a philanthropic family and unrestricted educational grants from Foundation partners Roche Products, Pty. Limited and Boehringer Ingelheim and Project partner Bristol-Myers Squibb Australia. This study is supported by an NHMRC grant no. APP1066128. H.E.J. has also received the Ivan-cash grant-in-aid from the LFA for completion of this project.