Journal article

Long-term outcomes of surgery for pulmonary artery sling in children

Matthew S Yong, Michael ZL Zhu, Douglas Bell, Nelson Alphonso, Johann Brink, Yves d'Udekem, Igor E Konstantinov

European Journal of Cardio-Thoracic Surgery | OXFORD UNIV PRESS INC | Published : 2019

Abstract

OBJECTIVES: Pulmonary artery (PA) sling is a rare vascular anomaly often associated with congenital tracheal stenosis. We describe the long-term outcomes with repair of this condition. METHODS: A retrospective study was conducted at 2 institutions. From 1984 to 2018, 33 patients with PA sling underwent repair. RESULTS: The median age at the time of surgery was 5.9 months (quartile 1-3: 2.5-12 months). Concomitant tracheal surgery was required in 21 patients (64%) where slide tracheoplasty was used in 11 patients (52%). There were no early deaths in patients who did not require tracheal surgery (n = 12). Operative mortality was 22% (2 of 9 patients) between 1984 and 1993, 11% (1 of 9 patients..

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Grants

Awarded by National Health and Medical Research Council (NHMRC) Postgraduate Scholarship


Funding Acknowledgements

M.S.Y. was supported by the David B. Rosenthal Scholarship (University of Melbourne), the Australian Government Research Training Program Scholarship and the National Health and Medical Research Council (NHMRC) Postgraduate Scholarship (APP1133977). Y.D. is a Career Development Fellow of the National Heart Foundation of Australia (CR 10M 5339), a Clinician Practitioner Fellow of the NHMRC (1082186) and is a consultant for the companies, MSD and Actelion.