Journal article

Left atrial cavernous haemangioma presenting with cardiac tamponade in a patient with Cowden syndrome

Alexandra Drucker, Chong Zhou, Siven Seevanayagam, Laurence Weinberg

BMJ CASE REPORTS | BMJ PUBLISHING GROUP | Published : 2019

Abstract

Cowden syndrome (CS) is a rare disorder characterised by multiple non-cancerous, tumour-like growths called hamartomas. The syndrome is associated with the development of cancer of the breast, endometrium, kidneys, skin and rarely the brain. We report a rare case of symptomatic cardiac haemangioma in a patient with CS. A 54-year-old woman with CS presented with dyspnoea and orthopnoea in the setting of cardiac tamponade. Echocardiography revealed a large haemopericardium and tamponade physiology, secondary to a pericardial mass. The patient underwent urgent cardiopulmonary bypass with removal of the mass. Histopathology confirmed a benign cavernous haemangioma. We postulate that tumours invo..

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University of Melbourne Researchers