Evaluation and Management of the Child and Adult With Fontan Circulation: A Scientific Statement From the American Heart Association.
Jack Rychik, Andrew M Atz, David S Celermajer, Barbara J Deal, Michael A Gatzoulis, Marc H Gewillig, Tain-Yen Hsia, Daphne T Hsu, Adrienne H Kovacs, Brian W McCrindle, Jane W Newburger, Nancy A Pike, Mark Rodefeld, David N Rosenthal, Kurt R Schumacher, Bradley S Marino, Karen Stout, Gruschen Veldtman, Adel K Younoszai, Yves d'Udekem Show all
Circulation | Published : 2019
It has been 50 years since Francis Fontan pioneered the operation that today bears his name. Initially designed for patients with tricuspid atresia, this procedure is now offered for a vast array of congenital cardiac lesions when a circulation with 2 ventricles cannot be achieved. As a result of technical advances and improvements in patient selection and perioperative management, survival has steadily increased, and it is estimated that patients operated on today may hope for a 30-year survival of >80%. Up to 70 000 patients may be alive worldwide today with Fontan circulation, and this population is expected to double in the next 20 years. In the absence of a subpulmonary ventricle, Fonta..View full abstract