Journal article

Path ahead for 'low risk' adolescents living with a Fontan circulation

David W Baker, Mark R Dennis, Diana Zannino, Chris Schilling, Patricia D Moreno, Andrew Bullock, Patrick Disney, Dorothy J Radford, Tim Hornung, Leeanne Grigg, Yves d'Udekem, Julian Ayer, David S Celermajer, Rachael Cordina



OBJECTIVE: A high risk of morbidity and mortality is well documented in adults with a Fontan circulation. The difference in outcomes between those with and without significant morbidity at the time of transition to adult care has not been well characterised. METHODS: We analysed clinical outcomes in patients enrolled in the Australian and New Zealand Fontan Registry ≥16 years of age. Low risk (LR) Fontan patients were defined as those without history of sustained arrhythmia, thromboembolic event, transplantation, Fontan conversion, protein-losing enteropathy, plastic bronchitis, New York Heart Association class III/IV and/or moderate/severe atrioventricular valve regurgitation or ventricular..

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