Reliability and validity of the FSHD-composite outcome measure in childhood facioscapulohumeral dystrophy
K de Valle, F Dobson, I Woodcock, K Carroll, MM Ryan, C Heatwole, K Eichinger, JL McGinley
NEUROMUSCULAR DISORDERS | PERGAMON-ELSEVIER SCIENCE LTD | Published : 2021
This study aims to investigate intra-rater reliability and construct validity of the Facioscapulohumeral Dystrophy Composite Outcome Measure (FSHD-COM), in childhood FSHD. Participants included eighteen children with FSHD, and matched healthy controls. Reliability data were collected from 15 participants with FSHD over two testing sessions. Validity data were collected from all participants. Participants with FSHD completed; the FSHD-COM (and modified pediatric version), Motor Function Measure-32 (MFM-32), FSHD Severity Scales, Performance of the Upper Limb 2.0, Pediatric Quality of Life™ Neuromuscular Module and pediatric FSHD Health-Index Questionnaire. Both versions of the FSHD-COM showed..View full abstract
Awarded by FSHD Global Research Foundation
This work was supported by FSHD Global Research Foundation - Grant 44.