Journal article

Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients

Matthew McKenzie, Michael Lazarou, David R Thorburn, Michael T Ryan

Journal of Molecular Biology | ACADEMIC PRESS LTD ELSEVIER SCIENCE LTD | Published : 2006

DOI: 10.1016/j.jmb.2006.06.057

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Keywords

Supercomplex
Membrane Protein
Genetic Diseases, X-Linked
Electrophoresis, Polyacrylamide Gel
Abnormalities
Life Sciences & Biomedicine
Mitochondria
Cardiolipins
Electron Transport Complex Iv
Proteins
Cardiolipin
Gene
Muscle Weakness
Humans
Linked Cardioskeletal Myopathy
Biochemistry & Molecular Biology
Mammalian Mitochondria
Mitochondrial Membranes
Biosynthesis
Electrophoresis
Science & Technology
Mutation
Cytochrome-C-Oxidase
Neutropenia
Cells, Cultured
Yeast
Blue Native Page
Membrane-Protein Complexes
Electron Transport Complex I
Cardiomyopathy, Dilated
Electron Transport Complex Iii
Transcription Factors
Syndrome
Lymphocytes
Infant