Journal article

A novel case of polyfibromatosis and interstitial granulomatous dermatitis with arthritis

Daniel Litu Chen, Alvin H Chong, Jack Green, David Orchard, Richard Williams, Laurence Clemens

Journal of the American Academy of Dermatology | MOSBY, INC | Published : 2006


Polyfibromatosis is a rare condition in which several cutaneous fibrotic conditions, such as Dupuytren's contracture, keloid formation, Peyronie's disease and plantar fibromatosis, may coexist. Interstitial granulomatous dermatitis with arthritis is also a rare condition characterized by arthritis and infiltrated rope-like lesions with granulomatous histologic features. We report a case of the simultaneous occurrence of both conditions in the same individual. To our knowledge, this has not been previously described. The clinical course has been slow, progressive, and recalcitrant to treatment.