Journal article

Dysarthria in Friedreich's Ataxia: A Perceptual Analysis

Joanne Folker, Bruce Murdoch, Louise Cahill, Martin Delatycki, Louise Corben, Adam Vogel



The aims of this study were to: (1) evaluate the perceptual speech dimensions, speech intelligibility and dysarthria severity of a group of individuals diagnosed with Friedreich's ataxia (FRDA); (2) determine the presence of subgroups within FRDA dysarthria; (3) investigate the relationship between the speech outcome and the clinical factors of disease progression. The study included 38 individuals (21 female, 17 male) with a confirmed diagnosis of FRDA. A group of 20 non-neurologically impaired individuals served as controls. Perceptual analysis, investigating 30 different dimensions of speech, was conducted on a speech sample obtained from each participant. In addition, the Assessment of I..

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Funding Acknowledgements

This project was funded by the Friedreich's Ataxia Research Alliance, USA, and the Friedreich's Ataxia Research Association, Australasia. The authors thank the participants involved in this study; Dr. Michael Fahey for administering the FARS; the Friedreich Ataxia Clinic, Monash Medical Centre, Vic., Australia, and the Friedreich's Ataxia Network, Qld., Australia, for recruitment. M. D. is an NHMRC practitioner fellow.