Journal article

The relative impact of vision impairment and cardiovascular disease on quality of life: The example of pseudoxanthoma elasticum

RP Finger, E Fenwick, M Marella, P Charbel Issa, HPN Scholl, FG Holz, EL Lamoureux

Health and Quality of Life Outcomes | BMC | Published : 2011

Abstract

Objective: To investigate the impact of pseudoxanthoma elasticum (PXE), a rare hereditary disease of concurrent vision impairment (VI) and cardiovascular complications (CVCs), on vision-related (VRQoL) and health-related quality of life (HRQoL).Methods: VRQoL and HRQoL were assessed using the Impact of Vision Impairment (IVI) questionnaire and the Short Form Health Survey (SF-36) in 107 PXE patients. Patients were stratified into four groups: A = no VI or CVC; B = CVCs only; C = VI only; and D = both VI and CVCs.Results: Following Rasch analysis, the IVI was found to function as a vision-specific functioning and emotional well-being subscale, and the SF-36 as a health-related physical functi..

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University of Melbourne Researchers

Grants

Awarded by Seventh Framework Programme


Funding Acknowledgements

Support: European Commission, FP7, Marie Curie Intra-European Fellowship (237238); University of Bonn BONFOR research grant and German Research Council grant (DFG FI 1540/5-1) to RPF. CERA receives Operational Infrastructure Support from the Victorian Government. RPF and EF had full access to all the data in the study and take responsibility for the integrity of the data and the accuracy of the data analysis.