Journal article
Impact of scoliosis surgery on activities of daily living in females with rett syndrome
J Downs, D Young, N De Klerk, A Bebbington, G Baikie, H Leonard
Journal of Pediatric Orthopaedics | Published : 2009
Abstract
BACKGROUND: Scoliosis is a common orthopaedic complication of Rett syndrome, and surgery is commonly used to reduce asymmetry in cases with severe scoliosis. METHODS: Data from questionnaires administered to caregivers biennially from 2000 to 2006 were used to describe functional skill levels in subjects with Rett syndrome, and within-subject change in 16 subjects with scoliosis surgery were compared with within-subject change in 186 pairs of data from 86 subjects with conservatively managed scoliosis. Postsurgical assessment was conducted after a mean of 17.8 months. RESULTS: Surgery was associated with improved activities of daily living as measured by the WeeFIM for subjects who were whee..
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Awarded by National Institute of Child Health and Human Development
Funding Acknowledgements
The authors would like to acknowledge the funding of the major aspects of the Australian Rett Syndrome program by the National Institutes of Health (5R01HD043100-05) and the National Health and Medical Research Council under project grant 303189 for certain clinical aspects. The authors would also like to acknowledge the support of the Rett Syndrome Association of Australia, the Australian Paediatric Surveillance Unit, and the Rett Syndrome Australian Research Fund. HL and NDK are funded by the National Health and Medical Research Council program grant 003209.