Outcomes of patients born with single-ventricle physiology and aortic arch obstruction: The 26-year Melbourne experience

Abstract

Background To review the long-term outcomes of patients born with single-ventricle physiology and aortic arch obstruction. Methods Follow-up of 70 consecutive neonates undergoing single-ventricle palliation and arch repair, excluding hypoplastic left heart syndrome, between 1983 and 2008, was reviewed. Dominant arch anomalies were coarctation (n = 48), interrupted arch (n = 10), and hypoplastic arch alone (n = 12). Neonatal Damus procedure with arch repair and shunt became the dominant approach, being performed in 1 (10%) of 10 in 1983 to 1989, 9 (32%) of 28 in 1990 to 1999, and 23 (72%) of 32 in 2000 to 2008. Results All patients underwent an initial procedure at a median of 6 days (range, ..